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#1Prion and Prion-Like Protein Strains: Deciphering the ... - NCBI
Increasing evidence is suggesting that prion-like proteins such as Aβ, α-synuclein, tau and TDP-43 share not only the prion replication paradigm ...
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#2Prions and Prion-like Proteins - Journal of Biological Chemistry
Prions are self-replicating protein aggregates and are the primary causative factor in a number of neurological diseases in mammals. The prion protein (PrP) ...
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#3In silico Characterization of Human Prion-Like Proteins
Human prion-like proteins constitute a subset of modular polypeptides broadly expressed across different cell types and tissues, significantly ...
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#4Prion - Wikipedia
Prions are a type of intrinsically disordered protein, which change their conformation unless they are bound to a specific partner such as another protein. With ...
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#5The propagation of prion-like protein inclusions in ...
Prions are infectious proteins whose ability to propagate results from their b-sheet-rich conformation converting the prion protein to the aberrant form through ...
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#6Prion-Like Proteins in Phase Separation and Their Link to ...
由 ML Sprunger 著作 · 2021 · 被引用 3 次 — Prions, or proteinaceous infectious particles, are a unique class of proteins [14]. A salient feature of prions is their infectious nature, characterized as ...
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#7Prion-like protein spotted in bacteria for the first time | Nature
A section of a protein in Clostridium botulinum, the microbe that causes botulism, can behave like a prion when it is inserted into yeast and ...
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#8Prion-like spreading of Alzheimer's disease within the brain's ...
The prion hypothesis states that misfolded proteins can act as infectious agents that template the misfolding and aggregation of healthy ...
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#9The Role of Functional Prion-Like Proteins in the Persistence ...
Prions are proteinaceous infectious agents that were discovered in the 1980s by Stanley Prusiner while studying Creutzfeldt–Jakob disease (Prusiner 1982).
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#10Natural and pathogenic protein sequence variation affecting ...
Impaired proteostatic regulation of proteins with prion-like domains (PrLDs) is associated with a variety of human diseases including ...
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#11Evolutionary behaviour of bacterial prion-like proteins - PLOS
Prion -like proteins are a small fraction of bacterial proteomes (Table 1). The largest fractions of NQID proteins are in the Mycoplasma genus ( ...
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#12(PDF) Prions and Prion-like Proteins - ResearchGate
The prion protein (PrP) undergoes a conformational transformation leading to aggregation into an infectious cellular pathogen. Prion-like ...
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#13The spread of prion-like proteins by lysosomes and tunneling ...
The prion-like nature of NDs. Seeding. The phenomenon of infectious template-mediated protein conversion is well described for prion diseases, a group of ...
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#14Prion-like disorders - Perelman School of Medicine at the ...
Moreover, two RNA-binding proteins, FUS and TDP-43, which form cytoplasmic aggregates in amyotrophic lateral sclerosis, harbor a 'prion domain' similar to those ...
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#15Intercellular Transmission of a Synthetic Bacterial Cytotoxic ...
Proteotoxic amyloid seeds can be transmitted between mammalian cells, arguing that the intercellular exchange of prion-like protein ...
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#16from computational approaches to proteome‐wide analysis
Moreover, it identified amyloid cores in PAPA synthetic prions and disease-related mutations in human prion-like proteins and the lack of them ...
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#17Prion-like protein acts as water sensor in seeds - National ...
The protein, named FLOE1, is usually dispersed throughout a seed. But when exposed to water, FLOE1 molecules rapidly condense to form blobs, ...
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#18Recent progress in prion and prion-like protein aggregation
Beyond infectious prions, the notion of prion-like spreading of misfolded conformations of proteins linked to neurodegenerative diseases has ...
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#19Targeting prion-like protein spreading in neurodegenerative ...
Zhang Z, Nie S, Chen L. Targeting prion-like protein spreading in neurodegenerative diseases. Neural Regen Res 2018;13:1875-8 ...
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#20Prion and Prion-like Proteins - Stanford EH&S
Prions and prion-like proteins call for Biosafety oversight. They are defined as human or animal proteins that meet any of the following criteria:.
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#21vesicle-mediated export and transmission of prion-like proteins
PRION -LIKE PROTEINS ARE VECTORS OF HERITABLE TRAITS IN YEAST AND NEURODEGENERATIVE DISEASES IN HUMANS. “Proteinaceous infectious particles”, or ...
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#22Prion‐like protein aggregates exploit the RHO GTPase to ...
A prion is a proteinaceous infectious particle which can propagate its misfolded and pathogenic conformation by corrupting the normally soluble ...
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#23Significance of Prion and Prion-Like Proteins in Cancer ...
New research in this area has demonstrated that PrP is over-expressed in a variety of cancers including gastric, pancreatic and breast cancers, affecting the ...
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#24The Prion-like Protein Finder
PrionW predicts proteins containing Q/N rich prion domains (PrDs) and identifies the 21-residues amyloid cores nucleating their amyloid formation.
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#25Discovering Prion-like Proteins in Eukaryotic Viruses - News ...
Prions are proteins that are known to have some unique features. They differ slightly in structure from regular proteins and are self- ...
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#26Complex networks of prion-like proteins reveal cross talk ...
Prions were first identified as the infectious protein agents causative of Creutzfeldt-Jakob disease or bovine spongiform encephalopathy ...
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#27Prion-like protein doppel Recombinant Protein - Cat. No. 92-424
Prion -like protein doppel Recombinant protein (Cat. No. 92-424) has been validated for use in biological assays.
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#28Polymorphisms within the prion (PrP) and prion-like protein ...
Polymorphisms within the prion (PrP) and prion-like protein (Doppel) genes in AD. Katell Peoc'h, AP-HP et Paris 5, Service de Biochimie, ...
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#29Full article: Prion-like proteins and their computational ...
We review here the role of prions, prionoids and prion-like proteins in health and disease, with a special focus on the algorithms and databases developed for ...
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#30Infectivity versus Seeding in Neurodegenerative Diseases ...
Essentially, any protein could show a prion-like propagation if it were able to acquire a characteristic folding that could be induced to other surrounding ...
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#31Amyloid Properties of Asparagine and Glutamine in Prion-like ...
由 Y Zhang 著作 · 2016 · 被引用 23 次 — Amyloids are fibrillar protein aggregates rich in β-sheet structures that can self-propagate through protein-conformational chain reactions.
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#32Prnd - Prion-like protein doppel precursor - UniProt
Prion -like protein doppel ... protein homooligomerization Source: InterPro ... Post-translational modification: synthesis of GPI-anchored proteins ...
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#33Role of prion-like proteins in cell fate and memory - GtR - UKRI
We discovered that some of these proteins could adopt another state that we termed mnemon. Mnemons, like prions, adopt a new shape. In the case of the protein ...
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#34Prion Diseases | Johns Hopkins Medicine
A prion is a type of protein that can trigger normal proteins in the ... This is an infectious type of the disease that is related to “mad cow disease.
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#35Prion-like protein found in plants - ScienceDaily
Prion -like protein found in plants ... Whitehead Institute scientists have determined that a plant protein involved in the timing of flowering ...
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#36Home page - Prion-like protein - www6.inra.fr
Prion -like protein. Researchers from IVPC have recently discovered that a virus affecting ruminants in Africa can form amyloid-like fibrils ...
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#37SARS-CoV-2 Prion-Like Domains in Spike Proteins Enable ...
Compared with other viruses, a striking difference was observed in the distribution of prion-like domains in the spike protein, since SARS-CoV-2 ...
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#38Prion-like protein Doppel Gene Set - Ma'ayan Laboratory ...
Genes. 1 proteins predicted to have the Prion-like protein Doppel protein domain from the InterPro Predicted Protein Domain Annotations dataset.
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#39Prion-like proteins drive several diseases of aging
In Nature, Walker and Jucker describe how prion-like protein aggregates drive the progression of several neurodegenerative diseases.
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#40Long-term Memories Are Maintained by Prion-like Proteins
In four papers published in Neuron and Cell Reports, Dr. Kandel's laboratory show how prion-like proteins – similar to the prions behind mad ...
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#41A prion-related protein senses warmer temperature in plants
While prions were first identified for causing disease in humans, proteins with prion-like sequences are very common and found across the ...
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#42The cell biology of prion-like spread of protein aggregates
By seeding misfolding of the PrP C (normal conformer prion protein) into PrP Sc (abnormal disease-specific conformation of prion protein), prions ...
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#43Tau Protein and Prion-Like Properties - Bio-Bits - BioLegend
investigated the ability of tau protein to exhibit prion-like functions. BioLegend provides an excellent selection of tau antibodies and recombinant proteins to ...
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#44Prion-like protein found in plants | Whitehead Institute
Whitehead Institute scientists inserted the Arabidopsis thaliana protein Luminidependens (LD) into yeast to determine whether it has the traits of a prion.
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#45Prying into the Prion Hypothesis for Parkinson's Disease
A key premise for the hypothesis that α-SYN acts as a prion-like protein in PD is that α-SYN assemblies, which can act as seeds for further ...
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#46Uncovering Unique Structural Features in Protein Regions ...
Prion -like domains have become a topic of interest because of their connection with a variety of debilitating brain diseases, ...
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#47Investigating the Spreading and Toxicity of Prion-like Proteins ...
Scientific Text Article | Prion-like propagation of protein aggregates has recently emerged as being implicated in many neurodegenerative ...
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#48Prion-like proteins as epigenetic devices of stress adaptation.
In addition to direct chromatin modifications, prion-like proteins have recently emerged as a system that can sense and adapt the cellular response to ...
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#49Do Vampire-Like Proteins Make Coronavirus More Contagious?
Prions are self-replicating proteins that cause infectious brain diseases. They have misfolded structures and, like zombies that turns people ...
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#50Prion Diseases | CDC
Prion diseases or transmissible spongiform encephalopathies (TSEs) are a family ... The abnormal folding of the prion proteins leads to brain damage and the ...
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#51Prion-like protein aggregation of desmin myofibrillar myopathies
This pathomechanism would be similar to neurodegenerative disorders and suggest a prion-like aggregate phenomenom in myopathies.
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#52Chapter 3: Prion-like Protein Seeding and the Pathobiology of ...
Alzheimer's disease (AD) and the amyloid (Aβ) cascade hypothesis. The prion paradigm. The prion paradigm and AD. Wide range of prion-like mechanisms.
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#53Prion-Like Protein Fights Off Viruses | HHMI
An immune defense protein uses prion-like qualities to fend off viruses. A cell must act fast to ward off a virus effectively: It must ...
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#54Targeting prion-like protein doppel selectively suppresses ...
Doppel, a prion-like protein, has recently been rediscovered as a TEC-specific surface marker with uncertain functions; doppel contains domains ...
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#55Prionlike Protein Spotted in Bacteria for First Time - Scientific ...
A section of a protein in Clostridium botulinum, the microbe that causes botulism, can behave like a prion when it is inserted into yeast ...
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#56Prion-like transmission of protein aggregates in ... - UC
'prion-like' manner and that disease progression is associated with the intercellular transfer of pathogenic proteins. The transfer of naked infectious ...
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#57Protein Misfolding in Prion and Prion-Like Diseases - IOS Press
ALS is a devastating neuromuscular disease caused by prion-like spread of misfolded proteins in the neuromuscular system. Familial mutations ...
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#58Prion-like protein doppel Protein-NP_036541.2 - PRND
Buy PRND protein, Prion-like protein doppel Protein-NP_036541.2 (MBS2889102) product datasheet at MyBioSource, Proteins. Application: ELISA (EIA), Western ...
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#59Spike protein可加速Prion-like protein聚集 - 人生沒有用不到的 ...
常見的腦神經退化疾病如阿茲海默症(Alzheimer's disease,AD)與巴金森氏症(Parkinson's disease,PD)是Prion-like protein聚集引發,分別為Tau ...
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#60A PRION-LIKE PROTEIN IS ESSENTIAL FOR LONG-TERM ...
The Science Explained. Prions may not be all bad, after all. Contrary to the widely held belief that unfolded prion proteins are toxic, scientists have made ...
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#61Prion-like protein is critical for long-term memory of the brain
Cell death release of prion protein, then it will be absorbed by other cells, and then infected prions, the abnormal prion protein as a cause of mad cow disease ...
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#62Prions: Protein Aggregation and Infectious Diseases
Fungal prions are non-PrP related molecules that include HET-s, Ure2p, and Sup35 ...
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#63Protein Misfolding: Prion-like Propagation and Cure ...
My long-term goal is to understand, how misfolded proteins, associated with the pathogenesis of most neurodegenerative diseases, propagate in a prion-like ...
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#64Memories Cemented by Flux of Prion-Like Proteins - Genetic ...
The new study—“The Persistence of Hippocampal-Based Memory Requires Protein Synthesis Mediated by the Prion-like Protein CPEB3”—appeared June 17 ...
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#65Human prion-like proteins and their relevance in disease
Yeast prions are proteins with the ability to switch between a soluble an amyloid state as an adaptive mechanism to confront environmental changes. Most of the ...
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#66Role of RNA Binding Proteins with prion-like domains in ...
Role of RNA Binding Proteins with prion-like domains in muscle and neuromuscular diseases – A number of neuromuscular and muscular diseases, ...
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#67Evolutionary behaviour of bacterial prion-like proteins
There are >60 prion-like protein domain families that have at least the evolutionary coverage of. Rho, and are found in multiple phyla. The ...
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#68Prion-like Protein Stabilizes Long-Term Memories in Mice
CPEB3 is a “prion-like” protein that may also contribute to neurodegenerative diseases including Alzheimer's, Parkinson's, and amyotrophic ...
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#69Prion-like Proteins Cause Disease | The Scientist Magazine®
Normal proteins with regions resembling disease-causing prions are responsible for an inherited disorder that affects the brain, muscle, ...
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#70Protein Folding, Prions, and Disease - iBiology
Susan Lindquist explains how prions provide a protein-based mechanism of inheritance that allows organisms to develop new traits, quickly and reversibly.
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#71Prion diseases: immunotargets and therapy | ITT - Dove ...
The 14-3-3 proteins are a family of conserved regulatory molecules and are increased in the cerebrospinal fluid. In the UK, familial prion ...
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#72Prions-What are they ? Protein Misfolding Mechanism
A prion is an infectious agent composed entirely of protein ... other prion proteins, leading to disease that is similar to viral infection.
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#73Prion protein and prion disease - YouTube
This lecture explains about the infectious agent called prion and the role of prion proteins in establishing diseases.
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#74Prions - YouTube
The protein it is composed of, called PrP (short for prion protein) can fold ... and natural selection just like other forms of replication.
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#75Prions | Institute for Neurodegenerative Diseases - UCSF
Prions (pronounced "PREE-ons") are formed from proteins normally present in the brain ... If you, a family member, or a friend have been diagnosed with CJD, ...
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#76Prion diseases - Deutsches Primatenzentrum
The infectivity of the prion proteins (red) is clearly visible in the movement of ... These are protein structures (not like viruses or bacteria of living ...
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#77Prion | Memory Alpha
In 2373, Julian Bashir was studying prion replication in ganglionic cell clusters. ... This radiation altered the conformation of prion-like protein in the ...
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#78Size of protein aggregates, not abundance, drives spread of ...
29 edition of the journal Science, researchers at Brown University report a key new insight into how prion proteins — the infectious agents — ...
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#79Call me Bond, Prion Bond - Scienceline
The protein is now a prion; the conversion is complete. Like good sleeper agents, the prion can lie dormant for a long period of time.
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#80PRION BASICS Prion Definitions
Antibody: a protein that fights infections. ... Ruminant: an animal (like a cow or sheep) that has more than one stomach and swallows food and then brings ...
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#81Prions: special proteins | All you need is Biology
The brain acquires a spongiform aspect, it means, an aspect like a sponge. This is due to accumulation of prion proteins in neurons, ...
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#82Nuvaxovid (Novavax) - Australian Government Department of ...
What's in the Novavax vaccine. Novavax is a protein-based vaccine. This type of vaccine contains part of the coronavirus spike protein. Your ...
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#83Understanding Structure and Function of the Prion in Order to ...
The image is a cartoon illustration of a human prion protein derived from ... It is composed of 253 number of amino acids like the normal ...
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#84Understanding Alzheimer's: Marc Vermulst Discusses ...
Researcher Marc Vermulst and his team have discovered how years of prion-like proteins cause neurodegenerative disorders.
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#85This family carried a rare mutation that should have been lethal
These mice carried the exact same genetic mutation as a family who lived ... “There are many diseases (including prion disease) where the ...
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#86The science behind Soylent Green: Eating people is a bad idea
The disease is caused by prions, which cause proteins in the brain to fold irregularly. Prions don't respond to temperatures at which meat ...
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#87Unit 3 Molecular Genetics Study Guide Isei - Gamer.no
Measuring quality of health care related processes became an ... related dementing disorders, with in-depth presentation of prion diseases, Pick's disease, ...
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#88How long do long-term memories last? - Sharenol
... subdivided into two different types: explicit (conscious) and implicit (unconscious) memory. Long-term Memories Are Maintained by Prion-like Proteins ...
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#89How the mRNA Covid-19 Vaccines suppress the innate ...
The protein can bind to the G4s in the RNA and both of them react. The theory is that the protein becomes prion-like. These prion proteins have ...
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#90Researchers hope to reduce spread of CWD - The Western ...
Chronic wasting disease (CWD) is caused by a structurally abnormal version of a protein called a prion, infecting the nervous systems and ...
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#91BIOMED: Infectious Disease IV Flashcards | Chegg.com
-the agent= composed primarily of a protein called prion. corona viruses. -diverse family of enveloped positive sense single stranded RNA viruses.
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#92What the CWD Bill Means for Deer and Deer Hunters
However, chronic wasting disease (CWD) is spreading like wildfire ... It's caused by a prion—a misfolded protein that accumulates in the ...
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#93Dancing Protein Clouds: Intrinsically Disordered Proteins in ...
The aggregated states of a few proteins have shown to exhibit (functional) prion-like behavior, in other words, the aggregates self-perpetuate and inherit ...
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#94Protein Solubility and Aggregation in Bacteria
... the final amyloid aggregate in a prion-like protein should at the same time display brittleness, a property that facilitates propagation.
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#95Advances in Genetics - 第 226 頁 - Google 圖書結果
Yeast prions and human prion-like proteins: sequence features and prediction methods. Cellular and Molecular Life Sciences, 71, 2047e2063.
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#96Inflammation in Parkinson's Disease: Scientific and Clinical ...
In 1916–1927 an epidemic of an influenza-like illness ravaged Europe and North America. ... that SNCA has attributes that are common to prion-like proteins, ...
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